Search on: FACTOR VII DEFICIENCY 
Descriptors Found: 1
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Descriptor English:   Factor VII Deficiency 
Descriptor Spanish:   Deficiencia del Factor VII 
Descriptor Portuguese:   Deficiência do Fator VII 
Synonyms English:   Hypoproconvertinemia  
Tree Number:   C15.378.100.100.310
C15.378.100.141.310
C15.378.463.310
C16.320.099.310
Definition English:   An autosomal recessive characteristic or a coagulation disorder acquired in association with VITAMIN K DEFICIENCY. FACTOR VII is a Vitamin K dependent glycoprotein essential to the extrinsic pathway of coagulation. 
Indexing Annotation English:   DF: FACTOR VII DEFIC
History Note English:   85; was HYPOPROCONVERTINEMIA 1963-84 
Allowable Qualifiers English:  
BL blood CF cerebrospinal fluid
CI chemically induced CL classification
CO complications CN congenital
DI diagnosis DH diet therapy
DT drug therapy EC economics
EM embryology EN enzymology
EP epidemiology EH ethnology
ET etiology GE genetics
HI history IM immunology
ME metabolism MI microbiology
MO mortality NU nursing
PS parasitology PA pathology
PP physiopathology PC prevention & control
PX psychology RA radiography
RI radionuclide imaging RT radiotherapy
RH rehabilitation SU surgery
TH therapy US ultrasonography
UR urine VE veterinary
VI virology  
Record Number:   5268 
Unique Identifier:   D005168 

Occurrence in VHL:
 

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